This category includes disorders caused by prions, which are infectious proteins. Examples of the transmissible spongiform encephalopathies they cause include Creutzfeldt-Jakob Syndrome, Bovine Spongiform Encephalopathy, Gerstmann-Straussler-Scheinker Disease, Kuru, Scrapie in sheep and goats, Chronic Wasting Disease of cervids, Transmissible Mink Encephalopathy, and Fatal Familial Insomnia.
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3D Structure of Prion Protein
Technical explanation of sheep and human prion proteins in normal and dimer forms.
Kuru Information Page
Compiled by the National Institute of Neurological Disorders and Stroke (NINDS).
Prion propagation in vitro: are we there yet?
Analysis of prion disease progression in cellular and animal models. (May 01, 2008)
The Prion Protein Knockout Mouse
Paper by Andrew D Steele, Susan Lindquist and Adriano Aguzzi discussing the many phenotypes. (April 01, 2007)
Protein Misfolding in Prion Disease
Includes review of the pathogenesis of prion diseases. (May 16, 1997)
Molecular Evolution of Prions
Article about the different evolutionary pathways of bovids and humans. (May 09, 1996)
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Last update:April 26, 2013 at 5:35:06 UTC